Sample records for DEFECTO DE CAMPO RETICULAR (lattice defects)
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1

Theoretical and experimental study of the Suzuki-phase photonic crystal lattice by angle-resolved photoluminescence spectroscopy

Alija, Alfonso R.; Martínez Rodríguez, Luis Javier; Postigo, Pablo Aitor; Sánchez-Dehesa, José; Galli, Matteo; Politi, Alberto; Patrini, M.; Andreani, Lucio C.; Seassal, Christian; Viktorovitch, P.
2007-01-22

Digital.CSIC (Spain)

5

The behavior of mixed-metal oxides: Physical and chemical properties of bulk Ce1–xTbxO2 and nanoparticles of Ce1–xTbxOy

Wang, Xianqin; Hanson, Jonathan C.; Liu, Gang; Rodríguez, José A.; Iglesias Juez, Ana; Fernández García, Marcos
2004-09-15

Digital.CSIC (Spain)

7

Role of volume versus defects in the electrical resistivity of lattice-distorted V(001) ultrathin films

Huttel, Y.; Cerdá, J.I.; Martínez, J.L.; Cebollada, Alfonso

4 nm thick V layers grown by triode sputtering on MgO(001) single crystals and capped with MgO exhibit a perfect epitaxy accompanied by a tetragonal distortion and an unexpected volume compression that increases with the V deposition temperature. The electrical resistivity follows a deposition temp...

DRIVER (Spanish)

9

Phase delay and group velocity determination at a planar defect state in three dimensional photonic crystals

Galisteo López, J. F.; Galli, M.; Andreani, L. C.; Mihi Cervelló, Antonio Agustín; Pozas, R.; Ocaña Jurado, Manuel; Míguez García, Hernán Ruy
2007-03-08

Digital.CSIC (Spain)

10

Optical and morphological study of disorder in opals

Palacios Lidón, E.; Juárez, B. H.; Castillo Martínez, E.; López, C.
2005-03-01

Digital.CSIC (Spain)

13

Microporous crystalline zeolite material, zeolite ITQ-28, production method thereof and use of same

Corma Canós, Avelino; Sabater Picot, María José; Valencia, Susana
2005-04-07

Digital.CSIC (Spain)

14

Magnetization reversal and magnetic anisotropies in epitaxial Fe/MgO and Fe/MgO/Fe heterostructures grown on Si(001)

Martínez Boubeta, C.; Cebollada, Alfonso; Calleja, J. F.; Contreras, M. C.; Peiró, F.; Cornet, A.
2003-02-15

Digital.CSIC (Spain)

15

Lattice effects and current reversal in superconducting ratchets

Dinis, L.; Gonzalez, E.M.; Anguita, José Virgilio; Parrondo, J.M.R.; Vicent, J.L.

Competition between the vortex lattice and a lattice of asymmetric artificial defects is shown to play a crucial role in ratchet experiments in superconducting films. We present a novel and collective mechanism for current reversal based on a reconfiguration of the vortex lattice. In contrast to pre...

DRIVER (Spanish)

16

Lattice effects and current reversal in superconducting ratchets

Dinis, L.; González, E. M.; Anguita, José Virgilio; Parrondo, J. M. R.; Vicent, J. L.
2007-09-18

Digital.CSIC (Spain)

17

Large disparity between gallium and antimony self-diffusion in gallium antimonide

Bracht, H.; Nicols, S. P.; Walukiewicz, W.; Silveira, Juan Pedro; Briones Fernández-Pola, Fernando; Haller, E. E.
2000-11-02

Digital.CSIC (Spain)

18

Investigation of the origin of deep levels in CdTe doped with Bi

Saucedo, E.; Franc, J.; Elhadidy, H.; Horodysky, P.; Ruiz, C. M.; Bermúdez, V.; Sochinskii, N. V.
2008-05-01

Digital.CSIC (Spain)

19

Effect of doping method on microstructural and defect profile of Sb–BaTiO3

Brzozowski, E.; Caballero, A. C.; Villegas, Marina; Castro, M. S.; Fernández Lozano, José Francisco
2006-01-01

Digital.CSIC (Spain)

20

Distrofia corneal granular autosómica dominante causada por mutación del gen TGFBI en una familia mexicana/ Autosomal dominant granular corneal dystrophy caused by a TGFBI gene mutation in a mexican family

Zenteno, J.C.; Santacruz-Valdés, C.; Ramírez-Miranda, A.
2006-07-01

Resumen en español Objetivo: Las distrofias corneales son un grupo de alteraciones hereditarias en las que una acumulación progresiva de material amiloide, hialino o mixto en las distintas capas corneales produce disminución de la transparencia corneal. Se describen las características clínicas y los estudios moleculares del gen TGFBI en una paciente Mexicana con una distrofia corneal estromal de tipo granular. Métodos: Examen oftalmológico completo, caracterización fenotípica de la (mas) distrofia corneal, y análisis del gen TGFBI por reacción en cadena de la polimerasa (PCR) y por secuenciación nucleotídica, en DNA de la propósita y de un hermano afectado. Resultados: Las lesiones corneales observadas en la paciente fueron compatibles con el diagnóstico de distrofia corneal estromal de tipo granular (clásica). No se observaron lesiones en las otras capas corneales. El análisis del gen TGFBI en DNA de la paciente y de un hermano afectado reveló una mutación puntual, de adenina a guanina, en el exón 14 de TGFBI que origina un cambio de histidina a arginina en el aminoácido 626 (H626R) de la proteína TGFBI. Conclusiones: Éste es el primer caso en el que se demuestra que una distrofia corneal granular es causada por la mutación H626R en TGFBI. Esta mutación ha sido reportada consistentemente en la distrofia estromal de tipo empalizada, clínicamente diferente a la granular. Nuestros datos indican que existen excepciones en la aparente correlación genotipo-fenoitipo establecida en el grupo de distrofias corneales asociadas a mutación en el gen TGFBI. Resumen en inglés Objective: To describe the clinical data and the results of molecular analyses of the TGFBI gene in a patient with classic granular stromal corneal dystrophy (type I). Methods: A female patient aged 60-years complaining of a long-standing decrease of visual acuity bilaterally associated with photophobia and foreign body sensation, underwent a complete ophthalmologic examination. Molecular analyses of DNA from the patient and from an affected brother included PCR amplifica (mas) tion of exons 4, 11, 12, and 14 of the TGFBI gene and direct automated sequencing of the PCR products. Results: The affected patient showed a pattern of corneal stromal lesions that was compatible with a diagnosis of classic granular dystrophy. No involvement of other corneal layers was evident. Molecular analysis disclosed a point mutation in exon 14 of the TGFBI gene which consisted of an adenine to guanine change at nucleotide position 1924, predicting a substitution of arginine instead of histidine at residue 626 of the TGFBI protein (H626R). An identical mutation was detected in DNA from her affected brother. Conclusions: This is the first time that a case of stromal granular dystrophy has been demonstrated to be caused by the H626R mutation, a molecular defect classically detected in the phenotypically distinct lattice corneal dystrophy. Our data indicate that the same molecular defects in the TGFBI gene lead to different phenotypes in stromal dystrophies, thus expanding the genotypic-phenotypic spectrum in this group of corneal diseases.

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